Atypical presentation of antisynthetase syndrome – case report

Authors:

Irma Ovčina, Marina Vukčević, Boris Prodanović

Summary

Anti-synthetase syndrome is an autoimmune disease characterized by myositis and interstitial lung disease. In this paper we report on a middle-aged male patient with an uncommon anti-synthetase syndrome, presenting with pulmonary manifestation before myositis. It is important to identify these patients, because early diagnosis and appropriate treatment are essential for optimal care.

Sažetak
Antisintetazni sindrom autoimunosna je bolest koju karakteriziraju miozitis i intersticijska plućna bolest. U ovom radu prikazujemo sredovječnog pacijenta sa sindromom antisintetaze koji se, neuobičajeno, manifestirao plućnim promjenama prije miozitisa. Važno je da takvi bolesnici budu identificirani, jer su rana dijagnoza i odgovarajuće liječenje nužni radi optimalne skrbi za njih.

Vol.: 66

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